Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration.

Ferrara J, Gupta D, Foster E, Garman K, Stacy M
Mov Disord. 2008 23 (6): 875-8

PMID: 18361477 · DOI:10.1002/mds.21841

We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.

(c) 2008 Movement Disorder Society.

MeSH Terms (13)

alpha 1-Antitrypsin Deficiency Diagnosis, Differential Dyskinesias Dystonic Disorders Female Globus Pallidus Hepatolenticular Degeneration Humans Liver Cirrhosis Magnetic Resonance Imaging Middle Aged Oculomotor Muscles Substantia Nigra

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