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Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus.

Cohen D, Kutluay E, Edwards J, Peltier A, Beydoun A
Epilepsy Behav. 2004 5 (5): 792-6

PMID: 15380138 · DOI:10.1016/j.yebeh.2004.06.019

Creutzfeldt-Jakob disease (CJD) is a rare prion disease characterized by a spongiform encephalopathy in humans. Although the characteristic triad of myoclonus, dementia, and periodic EEG activity is easy to recognize, unusual manifestations of the disease may be challenging and create a diagnostic dilemma. We report a case of CJD that occurred in a 26-year-old patient who presented with a receptive (Wernicke's) aphasia secondary to nonconvulsive status epilepticus.

MeSH Terms (11)

Adult Aphasia, Wernicke Brain Creutzfeldt-Jakob Syndrome Electroencephalography Fatal Outcome Frontal Lobe Humans Magnetic Resonance Imaging Male Status Epilepticus

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